中文摘要：

极度高三酰甘油血症是继酗酒和胆石症后第三大常见的引起急性胰腺炎的病因，也是造成心血管事件的重要危险因素。由自身免疫性疾病引发的极度高三酰甘油血症临床上较为少见，给该疾病的诊断和治疗带来了一定的困难。所以，了解该疾病的临床特点、可能发病机制及相应治疗方法将为更加有效的治疗提供帮助，从而降低急性胰腺炎、心血管事件等并发症的风险，既提高患者的生存率，也改善了他们的生活质量。

英文摘要：

[Summary] Severe hypertriglyceridemia is the third common cause of acute pancreatitis following after alcohol abuse and cholelithiasis. Moreover, it is also an important risk factor of cardiovascular events. However, the cases of severe hypertriglyceridemia caused by autoimmune disease were rare in clinical, which would bring the difficulty for diagnosis and treatment. A better understanding of the clinical characteristics, possible pathogenesis, and corresponding therapy of the disease would be helpful, which would reduce the risk of complications, and finally improve both the survival rate as well as quality of life of these patients.