中文摘要：

目的：探讨听神经病谱系障碍伴耳鸣患者的耳鸣特征。方法：对14例听神经病谱系障碍伴耳鸣患者进行听力学检测和耳鸣情况评估,分析耳鸣程度与听力损失程度和听力曲线类型的相关性,并探讨性别、年龄、病程对耳鸣程度的影响。结果：1听神经病谱系障碍患者的耳鸣多在听力下降后3年内出现;2听神经病谱系障碍患者耳鸣发生率高,但严重程度多集中在轻中度水平;3耳鸣严重程度的主观分级与听力损失程度无明显相关性,听力损失曲线类型对耳鸣严重性的影响亦需进一步循证医学证据;4随着耳鸣病程的延长,耳鸣对生活影响的严重程度也随之增加;5噪声等危险因素可成为部分患者耳鸣加重的诱因。结论：本研究发现听神经病谱系障碍患者的耳鸣性状有其特有的临床特点,为进一步认识听神经病谱系障碍提供了临床依据。

英文摘要：

Objective：To investigate the characteristics of tinnitus in patients with auditory neuropathy spectrum disorder（ANSD）.Method：This study recruited 14 ANSD patients with tinnitus.All the ANSD patients underwent detailed history taking,audiological examinations and assessments of tinnitus.This study analyzed the correlation of tinnitus status and hearing loss,and discussed the effects of sex,age,and the course of disease on tinnitus in ANSD patients.Result：1In the ANSD patients,tinnitus often occurred in 3years after the onset of hearing loss;2Tinnitus was highly prevalent in ANSD patients,and the severity of tinnitus was mostly from mild to moderate;3There was no obvious correlation between the subjective grading of tinnitus and hearing loss degree,and the impact of curve patterns of hearing loss on the level of tinnitus need much more evidence-based proof;4Along with the course extension,the impact of tinnitus on the quality of life was much more obvious;5Some risk factors such as noise exposure could be the reasons of aggravating the degree of tinnitus.Conclusion：Tinnitus in ANSD patients has its unique clinical features.The study of Tinnitus in ANSD patients can provide clinical basis for further research in ANSD.